Friday

What is Hermansky-Pudlak Syndrome?

What is Hermansky-Pudlak Syndrome? GENETIC DISORDERS SERIES
What is Hermansky-Pudlak Syndrome?
Hermansky-Pudlak Syndrome (HPS)
is a rare inherited disease, named after two doctors in Czechoslovakia who, in 1959, recognized similar health conditions in two unrelated adults.Since the discovery of HPS, the condition has occurred all over the world but is most common in Puerto Rico.The most common health conditions with HPS are albinism, the tendency to bleed easily, and pulmonary fibrosis.To date, there have been eight different genes identified (HPS1HPS8).

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ADD IMMEASURABLY TO THE ENDURING VALUE OF YOUR CONFERENCE

ADD IMMEASURABLY TO THE ENDURING VALUE OF YOUR CONFERENCE A single speech of Ronald Reagan, the Great Communicator, drastically changed the world!Reagan's Time for Choosing speech in 1964 is the historic event that launched his magnificent political career.Smart words are more effective than smart bombs.For your conference, get a dynamic keynote speaker who can transform your people and your world.Take advantage of a unique libertarian orator, Basil Venitis.В As many a*sociations, colleges, industry groups, companies, political groups, lobbyists, professional congresses, and speakers bureaus have discovered, speeches by Basil Venitis add immeasurably to the enduring value of a conference.

Basil Venitis doesn't restate what you can learn from regular sources, but he stretches your imagination to new horizons.Venitis is extensively involved in policy issues and the Global Tax Revolt.He is often a part of the process, working to shape and direct critical components of libertarian issues.Venitis is a master of a colorful rhetoric enriched with alliterations, metaphors, heightened imagery, and emotional effect.Speeches by Basil Venitis enable audiences to truly learn, and provide fascinating, provocative insights and analysis, getting to the heart of the matter.It's no wonder that Venitis is so often called upon to present libertarian ideas and to clarify issues for the public.* Value.A single speech of Basil Venitis will be cherished by your conferees forever, guiding them at the crossroads of their lives and your organization, increasing their efficiency, and improving the good will of your organization.

* Access.When scheduling Venitis for your organization, you work directly with him to craft a keynote speech that fits your precise needs.Venitis works with organizations to ensure that his speeches provide maximum value, and he shares their dedication to making their conference a huge success.

* Insight.Given Venitis's great experience in speaking across the globe, and with his unparalleled knowledge of politics, economics, finance, sciences, philosophy, and spirituality, he can help you determine the keynote for your conference.

* Transformation.Your people will be transformed to a new level of knowledge, attitude, and organizational climate.

* Revamp.Your organization will be revamped with new soul, vision, and values.

* Affordability.The cost of having Venitis speak at your conference is negotiable, depending on place and time.Venitism is a new libertarian paradigm which integrates politics, economics, ethics, and spirituality.Venitists follow the Venitis Laws:

Venitis Law of Black Hole: Taxation is armed robbery that feeds the black h*le of political corruption; it's the perfect index of corruption and tyranny.Only evil governments tax citizens and companies.

Venitis Law of Constitution: The only purpose of a constitution is to protect citizens from government abuse.Reform treaties of a confederation not voted by the citizens are null and void.

Venitis Law of Democracy: Every democracy is eventually hijacked by rabblerousers, pullpeddlers, clans of kleptocrats, bumptious bugaboos, busybodies, butterbabies, nabobs of nepotism, cranks of cronyism, pusillanimous pu**yfooters, riffraffs of rascals, socialist sophists, and Machiavellian mafiosi.Democracy tends to kleptocracy.Anarchy should replace democracy.

Venitis Law of Depression: Only governments can cause economic depressions and funny money.Lower tax rates, a reduction in the burden of government, and elimination of kleptocracy and VAT are the only way to boost growth.

Venitis Law of Education: There is no direct relationship between education and schooling.You might be schooled but uneducated, and you might be educated but unschooled.Schools are concentration camps for the drones of society.В  Unschooling is much better than schooling.Internet is the best source of knowledge and information, replacing schools, libraries, media, parliaments, and postoffice.В  Venitis Law of Equality: Death is the only equalizer.Egalitarianism brings death to society, transforming citizens to zombies.В  You have to discover God your own way without intermediaries.God's truth should replace faith.

Venitis Law of Government: The only purpose of government is to protect citizens from criminals.Public services, central banks, and fiat money should be abolished.

Venitis Law of Heroism: Entrepreneurs, innovators, anarchists, and heretics are the real heroes.

Venitis Law of Insurance: Citizens with proper individual retirement accounts and health savings accounts should be allowed to opt out of State Insurance.

Venitis Law of Intervention: Any government intervention deteriorates an existing trend.Laissez-faire is the only progressive policy.

Venitis Law of Legislature: Parliaments should be abolished, because they continuously create laws that enslave citizens, constrain economic activity, loot producers, reward drones, and encourage political corruption.

Venitis Law of Misery: Throwing money to misery brings more misery.Fighting wild leverage with more leverage is homeopathic repression of reality.A deluge of fiat money brings financial plague and haemorrhage of economy.Real money is tied up to precious metals and strategic metals.В  Venitis Law of Property: Governments should not own or regulate any property, including electromagnetic waves.The first individual who improves or cultivates any unclaimed property is entitled to that property.В  Governments cannot own, allocate, regulate, or manipulate frequency fields and media.Eminent domain is null and
void.

Venitis Law of Religion: Religion is spiritual slavery.Church is the business of religion.Religious monopoly turns bishops to ayatollahs, and churches to Sodom and Gomor.В  Venitis Law of Selfownership: You own your body and your soul, and nobody should dictate what you take in and what you take out.Speech, education, heresy, habeas corpus, military service, mating, healthcare, abortion, cloning, drugs, guns, and euthanasia should be personal choices.

Venitis Law of Style: Your soul needs to resonate with mighty words and unique acts that express your style and destiny.Your government cannot dictate your language, your words, and your culture.Resonate now and sing your song!

Venitis Law of System: The most efficient political system is anarchy, where everything is private, there are no taxes at all, there is no government, and there is no parliament.

Venitis Square Law: Political corruption is proportional to the square of the size of the government.

Venitis Tax Law: Taxes destroy the economy.Raising tax rates is masochism.Smart stimulus is to cut tax rates.Stupidus stimulus is to increase spending, which stimulates the cancer of statism!
[zeezal] Latest Photographs In Beautiful Model Bipasha Basu

More minority babies

More minority babies Our nation is changing people.В  For example, white infants are on the verge of being displaced as the majority of newborns now that nearly half of babies in the USA are ethnic and racial minorities.You think that doesn’t scare the pants off the Tea Party.В  According to a story in USA Today:Only 50.2% of babies under age 1 are white and not Hispanic, according to the 2010 Census a sharp decline from 57.6% just 10 years earlier.»
alyson hannigan american pie 2

Thursday

PacNorWest

PacNorWest It's COLD up here.We were supposed to have driven the RV up here to visit friends and family on our way to the Sunflower State but, after giving that some serious thought and checking out last-minute ticket prices on line, we opted to fly up instead.Actually, some of us opted to fly.MacGyver, given the fact that it's been 2+ years since he last set foot in a cockpit and given the fact that he's going to have to hit the ground running (to the cockpit) once we arrive, opted to stay home and bury himself in the -10, the 5&9, and the MTP checklist/handbook that he has.Saved us wear and tear on the RV, 20+ hours of hard driving, and really only cost us about $150 more than driving up would have cost.


All in all, I think it was a wise decision.


So the kids and I are visiting while MacGyver studies.We're freezing while he bakes.It's chilly up here, even when it's warm.And SoCal is still experiencing quite a heatwave.One of the first things we did when we arrived was go SHOPPING.My poor children only had shorts and T shirts.So we hit up Kohl's, Target, and Fred Meyer.Oh, how I have MISSED Fred Meyer.During our time in Alaska, that and Sam's Club were the only evidence that civilization existed in Fairbanks.I spent many an hour with my baby girl in Fred's in Alaska.


Today we hit the Point Defiance Zoo with the cousins and had a great time!We've missed them and it's always good to reconnect with family.I did not bring a camera on this excursion so I don't really have pictures to post.The zoo was nice - the setting was gorgeous.And the fog burned off nicely to the point where I could actually say I was warm!Tomorrow is supposed to be even nicer!


I had to resist the urge to buy The Boy a Carhartt jacket.It was a great jacket and I had forgotten how much I love Carhartts.They are a staple in Alaska.But I couldn't justify spending $75 on a jacket for a 7 year old boy.So I didn't.It's very possible that we might wind up living over this way in the future so I'll think about it if and when that happens.


It's been great to hang with old friends here.It's a lot like going home.It was so hard to say goodbye to them in February so it's wonderful to be with them again.Almost like we're back in Hawaii, hanging out as usual.And it won't be AS hard to say goodbye to them this go-round because we'll be back in a few months for Christmas.So I'm not dreading it quite as much.


I'd write more but there is a Tempurpedic mattress along with a warm blanket calling my name.So I'm out!




Pau.




- hfs

Voters blame Bush more than Obama for the economy

Is it true that you can NOT blow lice eggs/nits away?

Is it true that you can NOT blow lice eggs/nits away? Is it true that you can NOT blow lice eggs/nits away?http://ping.fm/i1e96

MY COUSIN IS SLEEPING WITH MY WIFE в

{Thursday's Tip} Halloween Ep. 1

{Thursday's Tip} Halloween Ep. 1
Ok, so are yall ready for Halloween?I'm already getting excited for it and it’s August.we went with the Wizard of Oz theme..it seemed like the best "theme" to go with to fit all 4 of us.Luckily,В  my husband and I have always gone all out on Halloween and we almost always since we were dating dressed up for it!i'm lucky in that area b/c i realize most guys don't like to participate willingly!Anyways, I’ll be posting lots about fun little diy Halloween things so here is one to get you just as excited!!It will be a Thursday's 1.Working on a covered surface, coat each julep cup and candlestick with white primer spray paint.Let dry according to directions.Add a second coat if needed.

2.Coat items with fluorescent-yellow spray paint.Let dry according to directions.Add a second coat if needed.

K and the days of summer

**REPRINT** Elwell, John J. A medicolegal treatise on malpractice and medical evidence comprising the elements of medical jurisprudence by John J. Elwell. New York. Baker, Voorhis, 1871.**REPRINT**

**REPRINT** Elwell, John J. A medicolegal treatise on malpractice and medical evidence comprising the elements of medical jurisprudence by John J. Elwell. New York. Baker, Voorhis, 1871.**REPRINT** **REPRINT** Elwell, John J.A medicolegal treatise on malpractice and medical evidence comprising the elements of medical jurisprudence by John J.Elwell.New York.Baker, Voorhis, 1871.**REPRINT**








Orignal From: **REPRINT** Elwell, John J.A medicolegal treatise on malpractice and medical evidence comprising the elements of medical jurisprudence by John J.Elwell.New York.Baker, Voorhis, 1871.**REPRINT**


Voters blame Bush more than Obama for the economy